Cervical Ganglioneuroma in an 8 -Years Old Girl: A Rare Case Report

Atif Hafeez Siddiqui; Aqsa Sadaf; Syeda Yusra Hassan; Salman Ahmed; Shamsa; Syeda Fatima Naz Zaidi; Amber Shams

doi:10.70749/ijbr.v3i7.1866

Authors

Atif Hafeez Siddiqui Department of ENT Head and Surgery, Dow University Hospital, Karachi, Sindh, Pakistan.
Aqsa Sadaf Department of ENT Head and Surgery, Dow University Hospital, Karachi, Sindh, Pakistan.
Syeda Yusra Hassan Department of ENT Head and Surgery, Dow University Hospital, Karachi, Sindh, Pakistan.
Salman Ahmed Department of ENT Head and Surgery, Dow University Hospital, Karachi, Sindh, Pakistan.
Shamsa Department of ENT Head and Surgery, Dow University Hospital, Karachi, Sindh, Pakistan.
Syeda Fatima Naz Zaidi Department of ENT Head and Surgery, Dow University Hospital, Karachi, Sindh, Pakistan.
Amber Shams Liaquat University of Medical and Health Sciences, Jamshoro, Sindh, Pakistan.

DOI:

https://doi.org/10.70749/ijbr.v3i7.1866

Keywords:

Ganglioneuroma, Cervical mass, Pediatric neck tumor, Retropharyngeal mass, Neurogenic tumor

Abstract

Background: Ganglioneuroma is a rare, benign neurogenic tumor arising from sympathetic ganglia, most commonly located in the retroperitoneum and posterior mediastinum. Cervical involvement, especially in the retropharyngeal space, is exceedingly uncommon in the pediatric population. Case Presentation: We report the case of an 8-year-old female who presented with a progressive left-sided neck mass for one year, accompanied by dysphagia and muffled voice. Clinical examination revealed a 9 cm non-tender, mobile mass in the left neck region. Imaging showed a well-defined hypodense lesion extending from C1 to C5 within the left retropharyngeal, pre- and paravertebral space, causing airway narrowing. Surgical excision via a left retropharyngeal approach was performed without complications. Histopathological analysis confirmed the diagnosis of ganglioneuroma. Conclusion: Cervical ganglioneuroma is a rare differential diagnosis for pediatric neck masses. High clinical suspicion and early imaging are crucial for timely intervention. Surgical excision remains the treatment of choice, offering excellent outcomes.

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